Liver transplantation is a rare occurrence in patients with cystic fibrosis, and there are limited data on the benefits of such intervention. A recent study examined the outcomes of this procedure in children and adults with cystic fibrosis, reporting that a significant survival benefit can be achieved despite extrahepatic factors.
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Gridelli, B. Benefit of liver transplantation in patients with cystic fibrosis. Nat Rev Gastroenterol Hepatol 8, 187–188 (2011). https://doi.org/10.1038/nrgastro.2011.39
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DOI: https://doi.org/10.1038/nrgastro.2011.39