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  • Imaging Case Report
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Giant omphalocele, intrinsic duodenal obstruction

Journal of Perinatology volume 31, pages 293–295 (2011)Cite this article

Subjects

Patient 1 demonstrated duodenal atresia with a complete obstruction and a double bubble sign on the UGI. The patient was taken to the operating room, where duodenal atresia with an annular pancreas was found and she was treated with a duodenoduodenostomy. Unfortunately, she had a prolonged hospitalization complicated by continued poor feeding, prolonged parenteral nutrition, pulmonary hypoplasia, episodes of sepsis and died at 7 months of age.

Patient 2 was found to have a duodenal web on the UGI series. The patient was taken to the operating room, where the web was divided anteriorly to avoid injury to the sphincter of Oddi. This patient is alive and tolerating oral feedings at 3 months of age. The patient is treated with Phenobarbital for seizures probably related to hypoxic ischemic encephalopathy, but is hemodynamically stable, not requiring surgical intervention for Tetralogy of Fallot up to the current date.

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Authors and Affiliations

  1. Mallinckrodt Institute of Radiology, Washington University School of Medicine, St Louis, MO, USA

    T E Herman & M J Siegel

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  1. T E Herman
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  2. M J Siegel
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Correspondence to T E Herman.

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The authors declare no conflict of interest.

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Herman, T., Siegel, M. Giant omphalocele, intrinsic duodenal obstruction. J Perinatol 31, 293–295 (2011). https://doi.org/10.1038/jp.2010.163

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