Abstract
Congenital chylothorax (CC) can result from a congenital malformation or an acquired obstruction or disruption of the thoracic duct. Recently, oral administration of the phosphodiesterase-5 inhibitor, sildenafil, was reported to be effective in resolving non-pulmonary lymphatic malformations in infants and young children. We report a case of CC in a late preterm infant with congenital pulmonary lymphangiectasia where octreotide was not effective, but management with oral sildenafil was successful.
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Malleske, D., Yoder, B. Congenital chylothorax treated with oral sildenafil: a case report and review of the literature. J Perinatol 35, 384–386 (2015). https://doi.org/10.1038/jp.2015.10
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DOI: https://doi.org/10.1038/jp.2015.10
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