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Dental manifestations in severe combined immunodeficiency following bone marrow transplantation

Bone Marrow Transplantation volume 25, pages 1007–1009 (2000)Cite this article

Abstract

Severe combined immunodeficiency (SCID) is a rare primary immunodeficiency disorder with an estimated overall frequency of 1 in 75 000 live births. Bone marrow transplantation is the only curative treatment available. Using T cell-depleted HLA non-identical bone marrow requires preconditioning with a short course of cytotoxic chemotherapy. We report severe dental developmental anomalies in three such patients under long-term follow up. Bone Marrow Transplantation (2000) 25, 1007–1009.

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Authors and Affiliations

  1. Dept of Child Dental Health, Dental Hospital and School, Newcastle upon Tyne, UK

    BOI Cole & RR Welbury

  2. Children’s BMT Unit, Newcastle upon Tyne Hospitals NHS Trust, Newcastle upon Tyne, UK

    E Bond & M Abinun

Authors
  1. BOI Cole
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  2. RR Welbury
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  3. E Bond
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  4. M Abinun
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Cole, B., Welbury, R., Bond, E. et al. Dental manifestations in severe combined immunodeficiency following bone marrow transplantation. Bone Marrow Transplant 25, 1007–1009 (2000). https://doi.org/10.1038/sj.bmt.1702382

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  • DOI: https://doi.org/10.1038/sj.bmt.1702382

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