Abstract
We report the case of a 20-year-old female patient with Beckwith-Wiedemann syndrome presenting with high blood pressure and bilateral adrenal pheochromocytoma successfully removed with laparoscopy in the same time. To our knowledge, the present case is the first observation of a bilateral pheochromocytoma occurring in the Beckwith-Wiedemann syndrome. It provides further support for a genetic anomaly in this condition. Our case also indicates the interest of laparoscopy for the surgical treatment of adrenal pheochromo- cytoma, even in bilateral tumors.
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Bémurat, L., Gosse, P., Ballanger, P. et al. Successful laparoscopic operation of bilateral pheochromocytoma in a patient with Beckwith-Wiedemann syndrome. J Hum Hypertens 16, 281–284 (2002). https://doi.org/10.1038/sj.jhh.1001378
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DOI: https://doi.org/10.1038/sj.jhh.1001378
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