Abstract
Background A 61-year-old female with end-stage renal disease who was undergoing hemodialysis presented with an 8-week history of upper and lower extremity weakness associated with skin tightness and contractures.
Investigations Physical examination, blood analysis, electromyogram and skin biopsy.
Diagnosis Nephrogenic fibrosing dermopathy/nephrogenic systemic fibrosis.
Management Methylprednisolone, thalidomide and physical therapy.
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Weiss, A., Lucia, M. & Teitelbaum, I. A case of nephrogenic fibrosing dermopathy/nephrogenic systemic fibrosis. Nat Rev Nephrol 3, 111–115 (2007). https://doi.org/10.1038/ncpneph0373
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DOI: https://doi.org/10.1038/ncpneph0373
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