This is a preview of subscription content, access via your institution
Relevant articles
Open Access articles citing this article.
-
Interorgan ammonia trafficking in liver disease
Metabolic Brain Disease Open Access 09 December 2008
Access options
Subscribe to this journal
Receive 51 print issues and online access
$199.00 per year
only $3.90 per issue
Buy this article
- Purchase on Springer Link
- Instant access to full article PDF
Prices may be subject to local taxes which are calculated during checkout
References
Shih, E. in The Metabolic Basis of Inherited Disease (eds Stanbury, J.B., Wyngaarden, J. B. & Fredrickson, D. S.) 362 (McGraw Hill, New York, 1978).
Levin, B. & Russell, A. Am. J. Dis. Child 113, 142 (1967).
Snyderman, S. E. et al. Pediatrics 56, 65 (1976).
Walser, M. et al. Clin.Sci.molec.Med. 53, 173 (1977).
Batshaw, M. L., Brusilow, S. & Walser, M. Pediatrics 58, 227 (1976).
Brusilow, S. W. & Batshaw, M. L. Lancet i, 134 (1979).
Brusilow, S. W., Valle, D. L. & Batshaw, M. L. Lancet ii, 452 (1979).
Batshaw, M. L. & Brusilow, S. W. J. Pediat. 97, 893 (1980).
Wiegard, C. et al. J. Pediat. 96, 142 (1980).
Snyderman, S. E. et al. J. Pediat. 95, 61 (1979).
Visek, W. J. Nutr. Rev. 37, 273 (1979).
Rajantie, F., Simell, O. & Perheentupa, J. Lancet i, 1219 (1980).
Oyanagi, K. et al. J. Pediat. 94, 255 (1979).
Valle, D., Walser, M. & Brusilow, S. W. J.clin.Invest. 65, 371 (1980).
Hommes, F. A. et al. Rep. int. Symp. on Metabolic Disease, Interlaken (1980).
Collins, F. S. et al. J. Pediat. 96, 429 (1980).
Bachmann, C. & Colombo, J. P. Eur. J. Pediat. 134, 109 (1980).
Stewart, P. M. & Walser, M. J.biol. Chem. 255, 5270 (1980).
Close, J. H. New Engl. J. Med. 290, 663 (1974).
McReynolds, J. W. et al. J. Pediat. 93 421 (1978).
Thoene, S. et al. J. Pediat. 90, 213 (1977).
Brusilow, S., Tinker, J. & Batshaw, M. L. Lancet ii, 432 (1979).
Brusilow, S., Thomas, G. H. & Brusilow, S. W. Pap. at Meet, on Inborn Errors of Metabolism, Florida (1980).
Smith, I. & Francis, D. E. M. in Textbook of Paediatric Nutrition (eds McLaren, D. & Burman, D.) 273 (Churchill Livingstone, 1976).
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Smith, I. The treatment of inborn errors of the urea cycle. Nature 291, 378–380 (1981). https://doi.org/10.1038/291378a0
Issue Date:
DOI: https://doi.org/10.1038/291378a0
This article is cited by
-
Ornithine phenylacetate revisited
Metabolic Brain Disease (2013)
-
Interorgan ammonia trafficking in liver disease
Metabolic Brain Disease (2009)
-
Treating urea cycle defects
Nature (1981)