Table 2 Characteristics of the eight patients diagnosed at the institute of tuberculosis and lung diseases between 2012 and 2019.

From: Molecular analysis of Pseudomonas aeruginosa strains isolated from cystic fibrosis patients

Mean age, years (SD) 30,3 (10,9)
Median age of diagnosis, years (SD) 8,8 (7,8)
Sex, males/females 3/5
CFTR classificationa
del F508 homozygous, N (%) 3 (37,5)
del F508 heterozygous, N (%) 3 (37,5)
Other, N (%) 2 (25,0)
Comorbidities
Pancreatic insufficiency (%)b 6 (75,0)
Cystic fibrosis-related diabetes (%)c 4 (50,0)
FEV1% predicted; mean (SD) 45,3 (18,9)
FVC1% predicted; mean (SD) 61,8 (14,4)
BMI; median (IQR) 18,9 (18,3–19,8)
  1. aHomozygous: both alleles containing the delta F508 mutation; Heterozygous: one allele containing the delta F508 mutation; Other: alleles containing mutations that are different.
  2. bPancreatic insufficiency: use of pancreatic enzymes.
  3. cCystic fibrosis-related diabetes: use of insulin.