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Use of transcranial motor evoked potentials (TcMEPs) in spine deformity surgery in a case of Charcot-Marie-tooth disease—what we should know? A case report

Spinal Cord Series and Cases volume 10, Article number: 38 (2024) Cite this article

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Abstract

Introduction

Charcot Marie tooth disease (CMTD) is also known as Hereditary sensory motor neuropathy. It poses difficulties in attaining intra-operative neuromonitoring signals for deformity correction surgery. In this case report, we intent to mention key points for obtaining good neuromonitoring signals in these cases which increases the safety in scoliosis surgery.

Case presentation

We present a 14-year-old boy, known case of CMTD, presented with progressive deformity of the back. The child was wheelchair-bound and could walk only a few steps with support. He was unable to maintain a sitting balance without using upper limbs making him functionally quadriparatic. The radiographs showed a double scoliotic curve with costo-pelvic impingement. At the onset, no signals were obtained with routine intra-operative neuromonitoring settings.

Discussion

Increasing the sweep length and voltage in our neuro-monitors helped in acquiring the baseline signals and we went ahead to proceed the deformity correction.

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Fig. 1: Plain radiographs.
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Authors and Affiliations

  1. Department of Spine Surgery, Max Superspeciality Hospital, Vaishali, Ghaziabad, India

    Abhishek Srivastava, Anuj Gupta & Arvind Jayaswal

  2. Department of Spine Surgery, Kothari Medical Center, Kolkata, India

    Vikas Hanasoge

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  1. Abhishek Srivastava
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  2. Vikas Hanasoge
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  3. Anuj Gupta
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  4. Arvind Jayaswal
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Contributions

AS was responsible for proofreading the manuscript. VH was responsible for literature search and writing case presentation in the manuscript. AG was responsible for writing the Introduction, Discussion, and conclusion part of the manuscript and also submitting and responding to the reviewer’s comments. AJ was responsible for proof reading the manuscript.

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Correspondence to Anuj Gupta.

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Srivastava, A., Hanasoge, V., Gupta, A. et al. Use of transcranial motor evoked potentials (TcMEPs) in spine deformity surgery in a case of Charcot-Marie-tooth disease—what we should know? A case report. Spinal Cord Ser Cases 10, 38 (2024). https://doi.org/10.1038/s41394-024-00648-z

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