Intracardiac leiomyomatosis: iliac vein to right-ventricular outflow tract

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Abstract

Background A 58-year-old female with a history of hypertension and asthma presented to an internist for a routine physical examination. A grade II/VI systolic ejection murmur and electrocardiogram abnormalities were noted. She was referred to a cardiologist for further assessment.

Investigations Transthoracic echocardiography, transesophageal echocardiography, contrast-enhanced CT and MRI, exploratory laparotomy.

Diagnosis Intracardiac leiomyomatosis.

Management Surgical excision.

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Figure 1: Transesophageal echocardiogram.
Figure 2: Gross pathologic specimen of leiomyoma measuring 30.0 cm in length, with a diameter ranging from 1.5 to 2.5 cm.
Figure 3: Microscopic examination of leiomyoma with focal hyalinization and myxoid degeneration.

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Correspondence to Icilma Fergus.

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The authors declare no competing financial interests.

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