Torsades de Pointes: A Rare Complication of an Extra-Adrenal Pheochromocytoma


Pheochromocytoma is an infrequent secondary cause of arterial hypertension, often associated with paroxysmal headache, sweating, weight loss, and palpitations. Cardiovascular complications of pheochromocytoma include sudden death, heart failure due to toxic cardiomyopathy, and hypertensive encephalopathy. Here we report the case of a female with an acquired long-QT-syndrome as a rare complication of an extra-adrenal pheochromocytoma. Diagnosis was made after sotalol-induced Torsades de Pointes.


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Correspondence to Heiko Methe.

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Methe, H., Hinterseer, M., Wilbert-Lampen, U. et al. Torsades de Pointes: A Rare Complication of an Extra-Adrenal Pheochromocytoma. Hypertens Res 30, 1263–1266 (2007).

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  • pheochromocytoma
  • long-QT-syndrome
  • Torsades de Pointes

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