Abstract
Epidermolysis bullosa acquisita (EBA) is now recognised as a histopathologically distinct condition.1-3 Ocular complications of hereditary epidermolysis bullosa (EB) have been well documented,4 but little has been reported with respect to the ocular manifestations associated with the acquired form.5-8
A patient with EBA and sarcoidosis - an association that does not appear to have been previously reported - developed spontaneous peripheral corneal melting and perforation. The defect healed with the use of a bandage contact lens, antibiotics, mydriatics and pulsed intravenous steroids, and resulted in a satisfactory visual outcome.
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Aclimandos, W. Corneal perforation as a complication of epidermolysis bullosa acquisita. Eye 9, 633–636 (1995). https://doi.org/10.1038/eye.1995.153
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DOI: https://doi.org/10.1038/eye.1995.153