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Perinatal/Neonatal Case Presentation

Congenital hepatic arteriovenous malformation: an unusual cause of neonatal persistent pulmonary hypertension


Congenital hepatic arteriovenous malformations are rare anomalies, which typically present in infancy with congestive heart failure, anemia, and hepatomegaly. Morbidity and mortality is high if the condition is not recognized and treated promptly. Hepatic arteriovenous malformation associated with persistent pulmonary hypertension of the newborn has been reported in two cases in the literature. We report a neonate who was referred for management of persistent pulmonary hypertension and was subsequently diagnosed with a large hepatic arteriovenous malformation. He underwent coil embolization following which pulmonary hypertension resolved.

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Correspondence to B G Sood.

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Alexander, C., Sood, B., Zilberman, M. et al. Congenital hepatic arteriovenous malformation: an unusual cause of neonatal persistent pulmonary hypertension. J Perinatol 26, 316–318 (2006).

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  • neonate
  • pulmonary hypertension
  • arterio-venous malformation
  • respiratory distress
  • hepatic
  • coil empolization

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