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Letter

Nature Genetics 28, 184–187 (1 June 2001) | doi:10.1038/88919

Germline mutations of the gene encoding bone morphogenetic protein receptor 1A in juvenile polyposis

James R. Howe , Jennifer L. Bair , Mohamed G. Sayed , Mary E. Anderson , Frank A. Mitros , Gloria M. Petersen , Victor E. Velculescu , Giovanni Traverso & Bert Vogelstein

Juvenile polyposis (JP; OMIM 174900) is an autosomal dominant gastrointestinal hamartomatous polyposis syndrome in which patients are at risk for developing gastrointestinal cancers. Previous studies have demonstrated a locus for JP mapping to 18q21.1 (ref.