Provider: Nature Publishing Group Content: application/x-research-info-systems TY - JOUR AU - Reddy, J.K. AU - Mannaerts, G.P. TI - Peroxisomal lipid metabolism JO - Annu. Rev. Nutr. PY - 1994/// VL - 14 SP - 343 EP - 370 M3 - 10.1146/annurev.nu.14.070194.002015 N1 - 10.1146/annurev.nu.14.070194.002015 UR - http://dx.doi.org/10.1146/annurev.nu.14.070194.002015 ER - TY - GEN AU - Mannaerts, G.P. AU - van Veldhoven, P.P. TI - Peroxisomes: Biology and Importance in Toxicology and Medicine PY - 1993/// ER - TY - GEN AU - Krisans, S.K. TI - Peroxisomes: Biology and Role in Toxicology and Disease PY - 1996/// ER - TY - JOUR AU - Subramani, S. TI - Protein import into peroxisomes and biogenesis of the organelle JO - Annu. Rev. Cell Biol. PY - 1993/// VL - 9 SP - 445 EP - 478 M3 - 10.1146/annurev.cellbio.9.1.445 N1 - 10.1146/annurev.cellbio.9.1.445 UR - http://dx.doi.org/10.1146/annurev.cellbio.9.1.445 ER - TY - JOUR AU - Subramani, S. TI - Protein translocation into peroxisomes JO - J. Biol. Chem. PY - 1996/// VL - 271 SP - 32483 EP - 32486 ER - TY - JOUR AU - Distel, B. TI - A unified nomenclature for peroxisome biogenesis factors JO - J. Cell Biol. PY - 1996/// VL - 135 SP - 1 EP - 3 M3 - 10.1083/jcb.135.1.1 N1 - 10.1083/jcb.135.1.1 UR - http://dx.doi.org/10.1083/jcb.135.1.1 ER - TY - JOUR AU - Braverman, N. AU - Dodt, G. AU - Gould, S.J. AU - Valle, D. TI - Disorders of peroxisome biogenesis JO - Hum. Mol. Genet. PY - 1995/// VL - 4 SP - 1791 EP - 1798 ER - TY - GEN AU - Wanders, R.J.A. AU - Barth, P.G. AU - Schutgens, R.B.H. AU - Tager, J.M. TI - Peroxisomes: Biology and Importance in Toxicology and Medicine PY - 1993/// ER - TY - GEN AU - Lazarow, P. AU - Moser, H. TI - The Metabolic Basis of Inherited Disease PY - 1989/// ER - TY - JOUR AU - Heymans, H.S.A. AU - Schutgens, R.B.H. AU - Tan, R. AU - van den Bosch, H. AU - Borst, P. TI - Severe plasmalogen deficiency in tissues of infants without peroxisomes (Zellweger syndrome) JO - Nature PY - 1983/// VL - 306 SP - 69 EP - 70 ER - TY - JOUR AU - Powers, J.M. TI - The pathology of peroxisomal disorders with pathogenetic considerations JO - J. Neuropathol. Exp. Neurol. PY - 1995/// VL - 54 SP - 710 EP - 719 ER - TY - JOUR AU - Evrard, P. AU - Caviness, V.S. AU - Prats-Vinas, J. AU - Lyon, G. TI - The mechanism of arrest of neuronal migration in the Zellweger malformation: an hypothesis based upon cytoarchitectonic analysis JO - Acta Neuropathol. PY - 1978/// VL - 41 SP - 109 EP - 117 ER - TY - JOUR AU - Dodt, G. TI - Mutations in the PTS1 receptor gene, PXR1, define complementation group 2 of the peroxisome biogenesis disorders JO - Nature Genet. PY - 1995/// VL - 9 SP - 115 EP - 125 M3 - 10.1038/ng0295-115 N1 - 10.1038/ng0295-115 UR - http://dx.doi.org/10.1038/ng0295-115 ER - TY - JOUR AU - Fransen, M. TI - Identification and characterization of the putative human peroxisomal C-terminal targeting signal import receptor JO - J. Biol. Chem. PY - 1995/// VL - 270 SP - 7731 EP - 7736 M3 - 10.1074/jbc.270.13.7731 N1 - 10.1074/jbc.270.13.7731 UR - http://dx.doi.org/10.1074/jbc.270.13.7731 ER - TY - JOUR AU - Wiemer, E.A.C. TI - Human peroxisomal targeting signal-1 receptor restores peroxisomal protein import in cells from patients with fatal peroxisomal disorders JO - J. Cell Biol. PY - 1995/// VL - 130 SP - 51 EP - 65 M3 - 10.1083/jcb.130.1.51 N1 - 10.1083/jcb.130.1.51 UR - http://dx.doi.org/10.1083/jcb.130.1.51 ER - TY - JOUR AU - Brocard, C. AU - Kragler, F. AU - Simon, M.M. AU - Schuster, T. AU - Hartig, A. TI - The tetratricopeptide repeat-domain of the PAS10 protein of Saccharomyces cerevisiae is essential for binding the peroxisomal targeting signal-SKL JO - Biochem. Biophys. Res. Commun. PY - 1994/// VL - 204 SP - 1016 EP - 1022 M3 - 10.1006/bbrc.1994.2564 N1 - 10.1006/bbrc.1994.2564 UR - http://dx.doi.org/10.1006/bbrc.1994.2564 ER - TY - JOUR AU - Baker, J. AU - Liu, J. AU - Robertson, E.J. AU - Efstratiadis, A. TI - Role of insulin-like growth factors in embryonic and postnatal growth JO - Cell PY - 1993/// VL - 75 SP - 73 EP - 82 M3 - 10.1016/0092-8674(93)90680-O N1 - 10.1016/0092-8674(93)90680-O UR - http://dx.doi.org/10.1016/0092-8674(93)90680-O ER - TY - JOUR AU - Powell-Braxton, L. TI - IGF-1 is required for normal embryonic growth in mice JO - Genes Dev. PY - 1993/// VL - 7 SP - 2609 EP - 2617 ER - TY - JOUR AU - Goldstein, J.L. AU - Brown, M.S. TI - Regulation of the mevalonate pathway JO - Nature PY - 1990/// VL - 343 SP - 425 EP - 430 M3 - 10.1038/343425a0 N1 - 10.1038/343425a0 UR - http://dx.doi.org/10.1038/343425a0 ER - TY - JOUR AU - Carlberg, M. TI - Mevalonic acid is limiting for N-linked glycosylation and translocation of the insulin-like growth factor-1 receptor to the cell surface JO - J. Biol. Chem. PY - 1996/// VL - 271 SP - 17453 EP - 17462 M3 - 10.1074/jbc.271.29.17453 N1 - 10.1074/jbc.271.29.17453 UR - http://dx.doi.org/10.1074/jbc.271.29.17453 ER - TY - JOUR AU - Fahimi, H.D. TI - Cytochemical localization of peroxidatic activity of catalase in rat hepatic microbodies (peroxisomes) JO - J. Cell Biol. PY - 1969/// VL - 43 SP - 275 EP - 288 M3 - 10.1083/jcb.43.2.275 N1 - 10.1083/jcb.43.2.275 UR - http://dx.doi.org/10.1083/jcb.43.2.275 ER - TY - JOUR AU - Wiemer, E.A.C. TI - Presence of peroxisomal membrane proteins in liver and fibroblasts from patients with the Zellweger syndrome and related disorders: evidence for the existence of peroxisomal ghosts JO - Eur. J. Cell Biol. PY - 1989/// VL - 50 SP - 407 EP - 417 ER - TY - JOUR AU - Espeel, M. TI - Immunolocalization of a 43 kDa peroxisomal membrane protein in the liver of patients with generalized peroxisomal disorders JO - Eur. J. Cell Biol. PY - 1995/// VL - 67 SP - 319 EP - 327 ER - TY - JOUR AU - Johnson, A.B. AU - Schaumburg, H.H. AU - Powers, J.M. TI - Histochemical characteristics of the striated inclusions of adrenoleukodystrophy JO - J. Histochem. Cytochem. PY - 1976/// VL - 24 SP - 725 EP - 730 ER - TY - JOUR AU - Powers, J.M. AU - Tummons, R.C. AU - Caviness, V.S. AU - Moser, A.B. AU - Moser, H.W. TI - Structural and chemical alterations in the cerebral maldevelopment of fetal cerebro-hepatorenal (Zellweger) syndrome JO - J. Neuropathol. Exp. Neurol. PY - 1989/// VL - 48 SP - 270 EP - 289 ER - TY - JOUR AU - Gressens, P. TI - Early neurogenesis and teratogenesis in whole mouse embryo cultures: histochemical, immunocytological and ultrastructural study of the premigratory neuronal-glial units in normal mouse embryo and in mouse embryos influenced by cocaine and retinoic acid JO - J. Neuropathol. Exp. Neurol. PY - 1992/// VL - 51 SP - 206 EP - 219 ER - TY - JOUR AU - Agamanolis, D.P. AU - Robinson, H.B.J. AU - Timmons, G.D. TI - Cerebro-hepato-renal syndrome; report of a case with histochemical and ultrastructural observations JO - J. Neuropathol. Exp. Neurol. PY - 1976/// VL - 35 SP - 226 EP - 246 ER - TY - GEN AU - Roels, F. TI - Functions and Biogenesis of Peroxisomes in Relation to Human Disease PY - 1995/// ER - TY - JOUR AU - Braverman, N. TI - Human PEX7 encodes the peroxisomal PTS2 receptor and is responsible for rhizomelic chondrodysplasia punctata JO - Nature Genet. PY - 1997/// VL - 15 SP - 369 EP - 376 M3 - 10.1038/ng0497-369 N1 - 10.1038/ng0497-369 UR - http://dx.doi.org/10.1038/ng0497-369 ER - TY - JOUR AU - Motley, A.M. TI - Rhizomelic chondrodysplasia punctata is a peroxisomal protein targeting disease caused by a non-functional PTS2 receptor JO - Nature Genet. PY - 1997/// VL - 15 SP - 377 EP - 380 M3 - 10.1038/ng0497-377 N1 - 10.1038/ng0497-377 UR - http://dx.doi.org/10.1038/ng0497-377 ER - TY - JOUR AU - Purdue, P.E. AU - Zhang, J.W. AU - Skoneczny, M. AU - Lazarow, P.B. TI - Rhizomelic chondrodysplasia punctata is caused by deficiency of human PEX7, a homologue of the yeast PTS2 receptor JO - Nature Genet. PY - 1997/// VL - 15 SP - 381 EP - 384 M3 - 10.1038/ng0497-381 N1 - 10.1038/ng0497-381 UR - http://dx.doi.org/10.1038/ng0497-381 ER - TY - JOUR AU - Motley, A. AU - Hettema, E. AU - Distel, B. AU - Tabak, H. TI - Differential protein import deficiencies in human peroxisome assembly disorders JO - J. Cell Biol. PY - 1994/// VL - 125 SP - 755 EP - 767 M3 - 10.1083/jcb.125.4.755 N1 - 10.1083/jcb.125.4.755 UR - http://dx.doi.org/10.1083/jcb.125.4.755 ER - TY - JOUR AU - Slawecki, M.L. TI - Identification of three distinct peroxisomal protein import defects in patients with peroxisome biogenesis disorders JO - J. Cell Sci. PY - 1995/// VL - 108 SP - 1817 EP - 1829 ER - TY - JOUR AU - Goldfisher, S. TI - Peroxisomal and mitochondrial defects in the cerebro-hepatorenal syndrome JO - Science PY - 1973/// VL - 182 SP - 62 EP - 64 ER - TY - JOUR AU - Tybulewisz, V.L. AU - Crawford, C.E. AU - Jackson, P.K. AU - Bronson, R.T. AU - Mulligan, R.C. TI - Neonatal lethality and lymphopenia in mice with a homozygous disruption of the c-abl proto-oncogene JO - Cell PY - 1991/// VL - 65 SP - 1153 EP - 1163 M3 - 10.1016/0092-8674(91)90011-M N1 - 10.1016/0092-8674(91)90011-M UR - http://dx.doi.org/10.1016/0092-8674(91)90011-M ER - TY - JOUR AU - Carmeliet, P. TI - Plasminogen activator inhibitor[ndash]1 gene-deficient mice: I. Generation by homologous recombination and characterization JO - J. Clin. Invest. PY - 1993/// VL - 92 SP - 2746 EP - 2755 ER - TY - JOUR AU - van Veldhoven, P.P. TI - Activity measurements of acyl-CoA oxidases in human liver JO - J. Inherited Metab. Dis. PY - 1995/// VL - 18 SP - 125 EP - 134 ER - TY - JOUR AU - Jones, K.M. AU - Hajra, A.K. TI - Assay of dihydroxyacetone phosphate acyltransferase with 32P-labeled substrate [letter] JO - Clin. Chem. PY - 1994/// VL - 40 SP - 946 EP - 947 ER - TY - JOUR AU - Vanhove, G. TI - Mitochondrial and peroxisomal [beta]-oxidation of the branched chain fatty acid 2-methylpalmitate in rat liver JO - J. Biol. Chem. PY - 1991/// VL - 266 SP - 24670 EP - 24675 ER - TY - JOUR AU - van Veldhoven, P. AU - Bell, R.M. TI - Effect of harvesting methods, growth conditions and growth phase on diacylglycerol levels in cultured human adherent cells JO - Biochim. Biophys. Acta PY - 1988/// VL - 959 SP - 185 EP - 196 M3 - 10.1016/0005-2760(88)90030-6 N1 - 10.1016/0005-2760(88)90030-6 UR - http://dx.doi.org/10.1016/0005-2760(88)90030-6 ER - TY - JOUR AU - Kaluzny, M.A. AU - Duncan, L.A. AU - Merritt, M.V. AU - Epps, D.E. TI - Rapid separation of lipid classes in high yield and purity using bonded phase columns JO - J. Lipid Res. PY - 1985/// VL - 26 SP - 135 EP - 140 ER - TY - JOUR AU - Blank, M.L. AU - Cress, E.A. AU - Piantadosi, C. AU - Snyder, F. TI - A method for the quantitative determination of glycerolipids containing o-alkyl and o-alk-1-enyl moieties JO - Biochim. Biophys. Acta PY - 1975/// VL - 380 SP - 208 EP - 218 M3 - 10.1016/0005-2760(75)90007-7 N1 - 10.1016/0005-2760(75)90007-7 UR - http://dx.doi.org/10.1016/0005-2760(75)90007-7 ER - TY - GEN AU - Moser, H.W. AU - Moser, A.B. TI - Techniques in Diagnostic Human Biochemical Genetics: A Laboratory Manual PY - 1991/// ER - TY - JOUR AU - Baumgart, E. AU - Volkl, A. AU - Hashimoto, T. AU - Fahimi, H.D. TI - Biogenesis of peroxisomes: immunocytochemical investigation of peroxisomal membrane proteins in proliferating rat liver peroxisomes and in catalase-negative membrane loops JO - J. Cell Biol. PY - 1989/// VL - 108 SP - 2221 EP - 2231 M3 - 10.1083/jcb.108.6.2221 N1 - 10.1083/jcb.108.6.2221 UR - http://dx.doi.org/10.1083/jcb.108.6.2221 ER - TY - GEN AU - Fahimi, H.D. AU - Baumgart, E. TI - Electron Microscopic Cytochemistry and Immunocytochemistry in Biomedicine PY - 1996/// ER - TY - GEN AU - Baumgart, E. TI - Peroxisomes PY - 1994/// ER - TY - JOUR AU - Fransen, M. AU - Brees, C. AU - van Veldhoven, P.P. AU - Mannaerts, G.P. TI - The visualization of peroxisomal proteins containing a C-terminal targeting sequence on Western blot by using the biotinylated PTS1-receptor JO - Anal. Biochem. PY - 1996/// VL - 242 SP - 26 EP - 30 M3 - 10.1006/abio.1996.0423 N1 - 10.1006/abio.1996.0423 UR - http://dx.doi.org/10.1006/abio.1996.0423 ER -