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  • Perinatal/Neonatal Case Presentation
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Perinatal/Neonatal Case Presentation

Amniotic band syndrome following septostomy in management of twin–twin transfusion syndrome: a case report

Journal of Perinatology volume 28, pages 377–379 (2008)Cite this article

Abstract

Septostomy, a rupture of the diamniotic membrane separating monozygotic twins essentially creating a monoamniotic gestation, is a potential therapeutic modality for twin–twin transfusion syndrome (TTTS). This may be associated with complications including cord entanglement or complete rupture of the membranes. We report a case of severe amniotic band syndrome with cord amputation after septostomy. A 33-year-old woman with a Mo-Di twin pregnancy was diagnosed with TTTS at 18 weeks of gestation. Septostomy as well as amnioreduction were performed at 24 weeks of gestation. A repeat cesarean delivery was performed at 31 weeks resulting in a live recipient baby of 1340 g and a dead donor with amniotic band syndrome. The donor showed pieces of membrane tightening both legs. The right thigh became entangled in the bands connecting to the umbilical cord of the live fetus. The umbilical cord of the dead twin was completely amputated, whereas the umbilical cord of the live infant was also entrapped within the amniotic band resulting in small diameter and some degree of stricture. This is the first report of a rare but serious complication following septostomy.

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Acknowledgements

We thank the babies and their parents for participating in the study. This study was supported by a grant from Health and Labour Sciences Research Grants: Comprehensive Research on Cardiovascular Diseases, no. 17160501 in Japan, which was entitled ‘Cohort study for concept, pathophysiology, establishment of diagnostic criteria, and effective intervention for metabolic syndrome in childhood’.

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Authors and Affiliations

  1. Department of Obstetrics and Gynecology, Maternal-Fetal Medicine Unit, Faculty of Medicine, Srinakharinwirot University, Bangkok, Thailand

    J Rujiwetpongstorn

  2. Department of Obstetrics and Gynecology, Faculty of Medicine, Chiang Mai University, Chiang Mai, Thailand

    T Tongsong

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  1. J Rujiwetpongstorn
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Correspondence to J Rujiwetpongstorn.

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Rujiwetpongstorn, J., Tongsong, T. Amniotic band syndrome following septostomy in management of twin–twin transfusion syndrome: a case report. J Perinatol 28, 377–379 (2008). https://doi.org/10.1038/sj.jp.7211927

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