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doi:10.1038/84818
Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits

Hélène Puccio Delphine Simon Mireille Cossée Paola Criqui-Filipe Francesco Tiziano Judith Melki Colette Hindelang Robert Matyas Pierre Rustin & Michel Koenig

This article appears in:
Nature Genetics 27, 181 - 186 (01 February 2001)
Nature Genetics 27, 181 - 186 (01 February 2001)

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